Cystic Fibrosis Organizations

Life expectancy for people with cystic fibrosis has steadily increased over the past 40 years. Some people with CF have serious lung and digestive problems. Others have a milder disease that does not show up until they are teenagers or young adults. CF is caused by a mutation in a gene called transmembrane conductance regulator in cystic fibrosis (CFTR). Respiratory failure is the most dangerous consequence of cystic fibrosis. In addition, the secretions block pancreatic enzymes that help digest fats and proteins, and they prevent your body from absorbing essential vitamins. The treatment of cystic fibrosis are aimed at relieving symptoms and complications.

The causes of cystic fibrosis

Common causes of cystic fibrosis:

Cystic fibrosis affects the mucous and sweat glands of the body and is caused by a defective gene.

Other bacteria may be involved.

Radiation, for example, after radiotherapy to other organs in the pelvis.

The main cause of fibrosis cystitis (and other urinary tract infections) is a bacteria known as coliform bacteria, which are a common occupant of the intestine.

The symptoms of cystic fibrosis

Some symptoms of cystic fibrosis:

Weight loss, or failure to gain weight normally in childhood.

Coughing or wheezing.

Fatigue.

Infants may have salty-tasting skin.

Recurrent respiratory infections such as pneumonia or sinusitis.

Stools that are pale or clay colored, foul odor, or float.

Diarrhea.

Stunting.

Cystic Fibrosis Treatment

Antibiotics for respiratory tract infections.

Vitamin supplements, especially vitamins A, D, E and K.

treatment with DNase enzyme replacement therapy. The drug dornase (Pulmozyme) contains an enzyme that thins the mucus and helps cough.

postural drainage and chest percussion.

Lung transplantation may be considered in certain cases.

Pancreatic enzymes to replace those missing.

Research has shown that ibuprofen may slow lung deterioration analgesic some children with cystic fibrosis. The results were most dramatic among children aged 5-13.